Acute Liver Failure Secondary to Hemophagocytic Lymphohistiocytosis during Pregnancy

نویسندگان

  • Jeanne-Marie Giard
  • Kerry A. Decker
  • Jennifer C. Lai
  • Ryan M. Gill
  • Aaron C. Logan
  • Oren K. Fix
چکیده

Hemophagocytic lymphohistiocytosis (HLH) is a syndrome of excessive immune activation that mimics and occurs with other systemic diseases. A 35-year-old female presented with signs of viral illness at 13 weeks of pregnancy and progressed to acute liver failure (ALF). We discuss the diagnosis of HLH and Kikuchi-Fujimoto (KF) lymphadenitis in the context of pregnancy and ALF. HLH may respond to comorbid disease-specific therapy, and more toxic treatment can be avoided.

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عنوان ژورنال:

دوره 3  شماره 

صفحات  -

تاریخ انتشار 2016